|Year : 2016 | Volume
| Issue : 1 | Page : 44-45
Huge Lipoblastoma in Neck
Vinit Kr Thakur1, Anju Singh2, Swati Singh3, Ramdhani Yadav1, Zaheer Hasan1, Vijayendra Kumar1
1 Department of Paediatrics Surgery, Indira Gandhi Institute of Medical Sciences, Sheikhpura, Patna, Bihar, India
2 Department of Pathology, Indira Gandhi Institute of Medical Sciences, Sheikhpura, Patna, Bihar, India
3 Department of Anaesthesiology & Critical Care, Indira Gandhi Institute of Medical Sciences, Sheikhpura, Patna, Bihar, India
|Date of Web Publication||12-Feb-2016|
Vinit Kr Thakur
Associate Professor, Dept. of Paediatrics surgery, IGIMS, Patna-14
Source of Support: None, Conflict of Interest: None
Lipoblastoma is not a rare entity in children. The more common sites are extremities and trunk. We report here a rare case of huge Lipoblastoma in neck region with axillary extension.
Keywords: Lipoblastoma, Huge, Neck
|How to cite this article:|
Thakur VK, Singh A, Singh S, Yadav R, Hasan Z, Kumar V. Huge Lipoblastoma in Neck. J Indira Gandhi Inst Med Sci 2016;2:44-5
| Introduction:|| |
Lipoblastoma,a fat cells benign tumor is encountered exclusively in infancy and young children.
Irrespective of it’s size and site, because of it’s benign nature complete surgical resection is possible with few recurrences. It is typically located in the extremeties, and presence of lipoblastoma in head and neck region ,trunk and various organs are encountered less frequently.
| Case Report:|| |
A 2yr old male child presented with a swelling in left side of neck. Three months back parents noticed a swelling that was small to start with, progressively increased in size over the period of time. There were no complains of pain,redness or discharge from the swelling. There was no other swelling elsewhere on the body. Family history was inconclusive.
Baby was active,healthy ,his milestones were developed as per age. On palpation there was a swelling of size 5x7cm in left supraclavicular region extending to left axillary region. Left clavicle could be well felt. Swelling was mobile and on compression it was more prominent in neck region.
Routine investigations were within normal limit and chest radiograph was normal. Ultrasound revealed a mass of lipomatous echotexture. Computed tomography suggested a soft tissue mass in neck ,which was extending to the axilla without involving neuro-vascular structures, mediastinal and intrathoracic extension were ruled out.
Mass was excised in toto from neck incision without any intra-operative or post-operative complication. The gross specimen measured 5x10cm and weighed around 200gm.lt was not encapsulated and appeared like bunch of grapes. Intraoperative specimen of Lipolastoma in neck.
Histopathological examination was suggestive of lobules of adipose tissue separated by fibrous septa. At places lipoblast were present. Background was myxoid ,nuclear atypia or giant cells were not noted.
The impression was suggestive of lipoblastoma. The patient recovered uneventfully and had no sign of recurrence 6months later.
| Disscussion:|| |
The term “lipoblast” was coined by Jaffe in 1926.. Lipoblastomas are usually well circumscribed. They can be diffuse, called lipoblastomatosis. They display identical histological features.2Adipose tissue tumors accounted for 6%of soft tissue tumor in paediatric population of which approximately 5-30% are lipoblastoma.,Less than 200 cases of lipoblastomas at various locations have been reported in literature 3. Cervical lipoblastomas are rare and represent 10 - 15%of all lipoblastomas cases. The present case is an unusual presentation of cervical lipoblastoma with axillary extension. Parents noticed mass in left lower neck. A review of 84 cases from the literature found that 61% of lipoblastoma occur in the extremities, followed by 15%on the trunk, 14%in the abdomen, and the head and neck region., Clinical examination and radiological evaluation gives idea about it’s pathology and surgical resection.,, The only definitive procedure for diagnosing a soft tissue mass is a histological analysis. The clinical course of lipoblastoma is benign, could grow locally to produce mass effect,
Complete excision usually leads to an excellent prognosis6,. In this case the swelling was huge and was present in neck with axillary extension, despite presence of major blood vessels and branchial plexus in vicinity it was completely excised without any complication. Local invasion and recurrences is not unheard of9. Though an aggressive surgery is not recommended ,the recurrence rate is between 0 and 25% if excision is incomplete. So complete excision is must for cure of this disease.
| Conclusion:|| |
lipoblastoma should be considered in a young child while evaluating soft tissue masses. Since it is a benign lesion complete resection is achievable irrespective of it’s size and site of occurrence.
| References|| |
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[Figure 1], [Figure 2]